Key Fact: Creutzfeldt-Jakob Disease. Number of confirmed or probable fatal cases in France. Data updated as of August 30, 2013.

A total of 27 confirmed or probable cases of vCJD have been identified in France. To date, all but the last case reported in 2012 have died. These 27 cases of vCJD have the following characteristics: they include 12 men and 15 women, with a median age at death or diagnosis of 36 years (between 19 and 58 years). Among them, 8 people resided in the Île-de-France region and 19 in other regions. For the 26 vCJD cases who died, deaths occurred in 1996 (1 case), 2000 (1 case), 2001 (1 case), 2002 (3 cases), 2004 (2 cases), 2005 (6 cases), 2006 (6 cases), 2007 (3 cases), 2009 (2 cases), and 2013 (1 case).All cases identified to date were homozygous Met-Met for codon 129 of the prion protein gene (PRNP); they had no identified risk factors for other recognized forms of CJD. One case had visited the United Kingdom very regularly for about ten years starting in 1987.